Hereditary Sensory And Autonomic Neuropathy Type 1b C1842586
An inherited nerve disorder causing progressive loss of sensation and autonomic dysfunction, usually appearing in adolescence. Management includes preventing injuries and treating symptoms.
Key facts at a glance
- ICD-10
- G43.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Sensory loss
(neurologic)Foot ulceration
(neurologic)Charcot arthropathy
(neurologic)Orthostatic hypotension
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Foot Care Protocol
Comprehensive daily foot inspection and care routine to prevent injuries and ulcers, including proper footwear selection and avoiding walking barefoot. Patient education on early wound recognition is essential.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Gait Training and Balance Exercises
Therapeutic exercises to improve balance and proper gait patterns, reducing fall risk and preventing ankle injuries. May include use of assistive devices.
Additional treatment options
Neuropathic Pain Management
Pharmacological approaches to manage burning or shooting pain associated with sensory neuropathy, typically using medications that target nerve pain pathways.
medicationWound Care and Debridement
Surgical management of infected ulcers or tissue necrosis that fails conservative treatment, including debridement and possible amputation for non-healing wounds.
surgicalRegular Neurological Assessments
Periodic comprehensive neurological examinations to monitor sensory loss progression and autonomic function changes.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Hereditary Sensory And Autonomic Neuropathy Type 1b C1842586?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy