Heterotaxy Visceral 4 Autosomal C3151057
A genetic disorder causing organs to develop on the wrong side of the body. It is inherited in an autosomal pattern with variable severity. Treatment depends on associated heart and organ defects.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Cardiac transposition
Midgut volvulus
Generalized symptoms
(congenital)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Abnormal organ laterality
(congenital)Pulmonary isomerism
(respiratory)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Heterotaxy-Specific Cardiac Reconstruction
Specialized surgical reconstruction tailored to the specific cardiac anatomy present in this heterotaxy variant. May include maze procedures for arrhythmias and valve repairs.
Targeted drug therapy with dose adjustment
Active treatment with regular monitoring by a healthcare provider is recommended.
Multidisciplinary Cardiac Follow-up
Coordinated care involving cardiology, cardiac surgery, and specialized nursing with regular follow-up appointments. Includes rhythm monitoring and functional assessments.
Additional treatment options
Electrophysiology Study and Ablation
Diagnostic and interventional procedures to identify and treat abnormal heart rhythms common in heterotaxy patients. Catheter ablation may be performed if arrhythmic foci are identified.
procedureCardiac-Specific Nutritional Support
Dietary modifications including sodium restriction, heart-healthy eating patterns, and appropriate fluid management. Nutritional supplementation may be needed if malabsorption is present.
dietaryActivity Modification and Cardiac Rehabilitation
Structured exercise programs adapted to cardiac capacity, with activity restrictions based on individual physiology. Cardiac rehabilitation provides supervised exercise training.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Heterotaxy Visceral 4 Autosomal C3151057?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Heterotaxy Visceral 4 Autosomal C3151057. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy