Hyperinsulinemic Hypoglycemia Familial 2 C2931833
A genetic disorder causing persistent low blood sugar due to uncontrolled insulin secretion. It can lead to seizures and developmental problems if untreated. Treatment includes diet modifications, medication, and sometimes surgical intervention.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complex Carbohydrate Meal Planning
Strategic meal composition emphasizing slow-release carbohydrates paired with protein and healthy fats to minimize postprandial insulin spikes and maintain euglycemia.
Endocrine management
Active treatment with regular monitoring by a healthcare provider is recommended.
Insulin Secretion Inhibitor
Pharmacological agent that directly suppresses pancreatic beta-cell insulin release by modulating ion channels, reducing the frequency and severity of hypoglycemic events.
Additional treatment options
Glucagon Emergency Protocol
Rescue medication administered during acute severe hypoglycemia to rapidly raise blood glucose through hepatic glycogenolysis, available in injectable and nasal forms.
medicationUncooked Cornstarch Supplementation
Slowly digestible complex carbohydrate administered before overnight fasting periods to provide sustained glucose release and prevent nocturnal hypoglycemia.
dietaryFocal Pancreatic Lesion Excision
Targeted surgical removal of discrete insulin-secreting adenomas within the pancreas, identified through specialized imaging and localization studies.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Hyperinsulinemic Hypoglycemia Familial 2 C2931833?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Hyperinsulinemic Hypoglycemia Familial 2 C2931833. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy