Hyperinsulinemic Hypoglycemia Familial 4 C1864948
A genetic condition where the pancreas produces too much insulin, causing recurrent low blood sugar. It typically manifests early in life and is managed with medications and dietary adjustments.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Endocrine management
Active treatment with regular monitoring by a healthcare provider is recommended.
Somatostatin Receptor Agonist
Long-acting injectable formulation that binds somatostatin receptors on pancreatic cells, suppressing glucagon and insulin secretion to maintain stable glucose levels.
Additional treatment options
Glucose Elevating Agent
Non-insulin hypoglycemic agent that stimulates hepatic glucose output while suppressing pancreatic insulin release through distinct molecular mechanisms.
medicationSelective Arterial Calcium Stimulation
Invasive localization procedure mapping insulin secretion gradients to identify focal disease within the pancreas, guiding surgical planning.
procedureFamily Psychoeducation Program
Structured educational intervention addressing the chronic stress of managing severe hypoglycemia, improving coping strategies and family functioning.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Hyperinsulinemic Hypoglycemia Familial 4 C1864948?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Hyperinsulinemic Hypoglycemia Familial 4 C1864948. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy