Immunodeficiency 96 C5676930
A rare genetic disorder affecting immune function. Patients are prone to frequent infections and typically require lifelong treatment focused on infection prevention and management.
Key facts at a glance
- ICD-10
- D89.9
- ICD-11
- 3A00.0
- Body system
- immunologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Severe persistent infections
Generalized symptoms
(immunologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Recurrent respiratory tract infections
(immunologic)Chronic diarrhea
(gastrointestinal)Arthralgia
(musculoskeletal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Immunoglobulin Replacement Therapy
Regular intravenous or subcutaneous immunoglobulin infusions to replace deficient antibodies and provide passive immunity against common pathogens. This foundational treatment reduces frequency and severity of infections.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Antibiotic Prophylaxis
Daily prophylactic antibiotics such as trimethoprim-sulfamethoxazole to prevent opportunistic infections, particularly Pneumocystis jirovecii pneumonia. Therapy is typically continued long-term.
Additional treatment options
Infection Prevention Measures
Comprehensive hand hygiene, avoidance of crowded indoor spaces, and respiratory precautions to minimize exposure to infectious agents. Patient education on recognizing early signs of infection.
lifestyleRegular Immunological Monitoring
Periodic assessment of immunoglobulin levels, infection frequency, and organ function to guide treatment adjustments and evaluate therapeutic response.
monitoringHematopoietic Stem Cell Transplantation
Curative approach involving replacement of defective immune cells through bone marrow or stem cell transplant from a matched donor. Reserved for severe cases or when standard therapy fails.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Immunodeficiency 96 C5676930?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy