Interstitial Lung Disease 1 C5562021
A condition where lung tissue becomes scarred and stiff, making breathing difficult. It can affect adults and children. Management includes medication, oxygen therapy, and lung rehabilitation.
Key facts at a glance
- ICD-10
- J98.9
- ICD-11
- CA00.0
- Body system
- respiratory
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Progressive dyspnea on exertion
(respiratory)Shortness of breath or cough
(respiratory)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Bibasilar crackles
(respiratory)Nonproductive cough
(respiratory)Digital clubbing
(respiratory)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Anti-fibrotic and Anti-inflammatory Therapy
Pharmacological treatment with antifibrotic agents and anti-inflammatory medications to slow disease progression and reduce pulmonary inflammation and fibrosis.
Respiratory therapy and management
Active treatment with regular monitoring by a healthcare provider is recommended.
Oxygen Therapy and Pulmonary Support
Supplemental oxygen therapy to maintain adequate oxygenation, improve exercise tolerance, and reduce pulmonary hypertension associated with advanced interstitial lung disease.
Additional treatment options
Pulmonary Rehabilitation Program
Comprehensive pulmonary rehabilitation including exercise training, breathing techniques, energy conservation strategies, and education to improve functional capacity and quality of life.
physical_therapyEnvironmental and Behavioral Modifications
Smoking cessation, avoidance of pulmonary irritants, infection prevention strategies, and activity pacing to reduce symptom exacerbation and disease progression.
lifestylePulmonary Function and Imaging Surveillance
Regular monitoring with pulmonary function tests, high-resolution CT imaging, and clinical assessments to track disease progression and treatment response.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Interstitial Lung Disease 1 C5562021?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Interstitial Lung Disease 1 C5562021. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy