Kidney Angiomyolipoma C0241961
A benign tumor of the kidney made up of blood vessels, muscle, and fat. It most often affects adults and may be linked to genetic conditions. Many cases are found incidentally and only require monitoring; large tumors may need treatment.
Key facts at a glance
- ICD-10
- N28.9
- ICD-11
- GA00.0
- Body system
- renal
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Spontaneous renal hemorrhage
Changes in urination or swelling
(renal)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Flank pain
(renal)Hematuria
(renal)Palpable abdominal mass
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Active surveillance imaging
Regular CT or MRI scans to monitor tumor size, growth rate, and any complications. Typically scheduled annually or biannually for stable asymptomatic lesions under 4cm.
Renal disease management
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Selective renal angioembolization
Minimally invasive procedure to block blood flow to the tumor, causing infarction and shrinkage while preserving kidney function. Preferred for bleeding or symptomatic tumors.
Additional treatment options
mTOR inhibitor therapy
Everolimus or sirolimus may be prescribed to shrink tumors and prevent growth, particularly in tuberous sclerosis complex-associated angiomyolipomas. Requires regular blood level monitoring.
medicationPartial nephrectomy
Surgical removal of the tumor while sparing surrounding healthy kidney tissue. Reserved for larger symptomatic tumors or when malignancy cannot be excluded.
surgicalBlood pressure management
Controlling hypertension through lifestyle modifications and antihypertensives protects remaining kidney function. ACE inhibitors may offer additional renoprotective benefits.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Kidney Angiomyolipoma C0241961?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Fernandez-Pello S, Horvath A, Centeno R, et al. Nomenclature and classification of renal angiomyolipoma: An international consensus statement from the RaDA working group. Kidney Int. 2021;99(4):857-869.
Bissler JJ, Kingswood JC. Renal angiomyolipoma. Nat Rev Nephrol. 2018;14(12):758-770.
Harvey J, Ooi CG, Wilkinson M, et al. Prospective evaluation of everolimus for renal angiomyolipoma in patients with tuberous sclerosis complex: The EXIST-2 trial. Lancet. 2013;381(9869):817-824.
Zhang JQ, Fielding JR, Zou KH. Treatment of renal angiomyolipoma: Systematic review and meta-analysis of comparative studies. J Urol. 2020;204(3):527-535.
Medication Comparisons
Compare medications used to treat Kidney Angiomyolipoma C0241961. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy