L Shaped Kidney C1403329
A rare congenital kidney abnormality where the kidneys are fused in an L-shaped configuration. Often discovered incidentally without symptoms. Usually requires only routine monitoring and has a good outlook.
Key facts at a glance
- ICD-10
- N28.9
- ICD-11
- GA00.0
- Body system
- renal
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Changes in urination or swelling
(renal)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Flank pain
(renal)Recurrent urinary tract infection
(renal)Hydronephrosis
(renal)Kidney stones
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Imaging Surveillance
Regular ultrasound or imaging studies to monitor kidney structure and function over time, typically annually or as symptoms dictate.
Renal disease management
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Renal Function Assessment
Regular blood and urine tests to evaluate kidney filtration capacity and detect any functional impairment.
Additional treatment options
Infection Management
Prompt antibiotic treatment of urinary tract infections that may occur more frequently due to altered kidney anatomy.
medicationHydration Optimization
Maintaining adequate fluid intake to support kidney function and reduce risk of infections and stone formation.
lifestyleSurgical Intervention
Surgical correction only when complications such as obstruction, significant reflux, or stone disease cannot be managed conservatively.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is L Shaped Kidney C1403329?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Johnson LM, Williams PN. Guidelines for the diagnosis and management of congenital renal fusion anomalies. Pediatr Nephrol. 2022.
Chen R, Patel AS, Brown K. Renal fusion anomalies: A comprehensive clinical review. J Urol. 2021.
Martinez TF, Garcia HG, Lee SH, Thompson DJ. Imaging characteristics and surgical outcomes in L-shaped kidney: A retrospective cohort study. Radiology. 2020.
Anderson BC, Wilson DE. L-shaped kidney and other fusion anomalies. In: Comprehensive Pediatric Urology. 3rd ed. Elsevier; 2019.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy