Long Qt Syndrome 1 C4551647
A genetic heart rhythm disorder where stress or exertion can trigger dangerous irregular heartbeats. Beta-blockers and activity restrictions help manage symptoms and prevent complications.
Key facts at a glance
- ICD-10
- I45.81
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Palpitations
(cardiovascular)Dizziness
(cardiovascular)Ventricular arrhythmia
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Non-Selective Beta-Blocker Therapy
High-dose beta-blockers as first-line treatment, particularly effective in LQT1 as exercise-triggered events are especially responsive to this therapy.
Swimming Restriction and Supervision
Strict avoidance of unsupervised swimming, a particularly dangerous trigger in LQT1 due to adrenergic surge during water immersion.
Additional treatment options
ICD Therapy
Defibrillator implantation for high-risk individuals including those with prior syncope or cardiac arrest, or inadequate response to beta-blockers.
procedurePotassium and Magnesium Supplementation
Optimization of electrolyte levels may help shorten QT interval in some patients with LQT1, particularly during illness or exercise.
complementaryPsychological Support for Anxiety Management
Counseling and support for patients and families dealing with diagnosis anxiety, particularly important for those with activity restrictions.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Long Qt Syndrome 1 C4551647?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Long Qt Syndrome 1 C4551647. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy