Lymphoma Hodgkin X Linked Pseudoautosomal C1846167
X-linked pseudoautosomal Hodgkin lymphoma is an extremely rare genetic form of Hodgkin lymphoma affecting males. It occurs due to genetic changes on the X chromosome and typically requires specialized treatment approaches. Management involves standard Hodgkin lymphoma protocols tailored to the genetic context.
Key facts at a glance
- ICD-10
- C80.1
- ICD-11
- 2A00.0
- Body system
- oncologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(oncologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Painless cervical lymphadenopathy
(lymphatic)Night sweats
(general)Pruritus
(integumentary)Alcohol-induced lymph node pain
(lymphatic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Chemotherapy regimen (ABVD or escalated BEACOPP)
Standard chemotherapy protocols using doxorubicin, bleomycin, vinblastine, and dacarbazine. Treatment intensity selected based on disease stage and risk stratification.
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Additional treatment options
Radiation therapy
Involved-site radiation therapy for early-stage disease or bulky presentations. Targets affected lymph node regions with precise dosing.
procedureImmunotherapy
Checkpoint inhibitor therapy for relapsed or refractory disease. Represents emerging standard of care for certain patient populations.
medicationStem cell transplantation
Autologous stem cell rescue for relapsed disease or high-risk presentations. Salvage chemotherapy followed by stem cell collection and reinfusion.
procedureLong-term follow-up and survivorship care
Ongoing surveillance for recurrence, secondary malignancies, and treatment-related complications. Includes cardiac, pulmonary, and thyroid screening.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Lymphoma Hodgkin X Linked Pseudoautosomal C1846167?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy