Moyamoya Disease 1 C2931384
Moyamoya disease is a rare condition where brain arteries narrow, reducing blood flow and forming fragile backup vessels. It can affect children and adults, potentially causing strokes. Treatment may include surgery to restore blood flow and medications.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Transient ischemic attacks (TIA)
Ischemic stroke
Seizures
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Headache
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Cerebral revascularization surgery
Direct or indirect bypass procedures such as STA-MCA anastomosis or encephaloduroarteriosynangiosis to restore cerebral blood flow and prevent stroke progression.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Additional treatment options
Antiplatelet therapy
Long-term antiplatelet medication to reduce thrombotic risk and prevent stroke in Moyamoya patients. Aspirin or similar agents may be used depending on clinical context.
medicationCerebrovascular imaging surveillance
Regular MRI/MRA or conventional angiography to monitor disease progression and assess collateral development. Helps guide timing of surgical intervention.
monitoringStroke prevention lifestyle modifications
Implementation of stroke prevention strategies including blood pressure control, avoiding extreme temperature exposure, maintaining hydration, and avoiding high-altitude activities.
lifestylePost-stroke rehabilitation
Intensive rehabilitation for patients with stroke or TIA including physical therapy, occupational therapy, and speech therapy as indicated by deficits.
physical_therapyWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Moyamoya Disease 1 C2931384?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Moyamoya Disease 1 C2931384. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy