Moyamoya Disease 3 C1837418
This genetic variant of Moyamoya disease involves progressive narrowing of brain arteries, creating compensatory fragile blood vessels. It affects both children and adults and may cause neurological symptoms. Treatment focuses on surgical revascularization.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Transient ischemic attacks (TIA)
Ischemic stroke
Seizures
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Headache
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Direct Bypass Surgery (STA-MCA)
Surgical revascularization procedure connecting the superficial temporal artery to the middle cerebral artery to restore blood flow to the brain.
Drug therapy with clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Antiplatelet Therapy
Long-term antiplatelet medication to reduce risk of ischemic events by preventing blood clot formation in narrowed vessels.
Additional treatment options
Regular Neuroimaging Surveillance
Periodic MRI and MRA or cerebral angiography to monitor disease progression and assess effectiveness of treatment interventions.
monitoringStroke Rehabilitation
Comprehensive rehabilitation program including physical, occupational, and speech therapy to address neurological deficits from ischemic events.
physical_therapyStroke Risk Factor Management
Aggressive management of modifiable risk factors including blood pressure control, smoking cessation, and avoiding extreme dehydration.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Moyamoya Disease 3 C1837418?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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Compare medications used to treat Moyamoya Disease 3 C1837418. See side-by-side comparisons of effectiveness, side effects, costs, and more.
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy