Moyamoya Disease 5 C3279690
A rare genetic form of Moyamoya disease affecting brain blood vessels, potentially causing reduced blood flow and stroke. This variant can impact both pediatric and adult populations. Surgical options may help restore adequate blood supply.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Transient ischemic attacks (TIA)
Ischemic stroke
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Headache
(neurologic)Cognitive impairment
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Indirect Bypass Surgery (EDAMS)
Encephaloduromyoarteriosynangiosis procedure where vascularized tissue is placed on the brain surface to promote new blood vessel formation over time.
Medication management with follow-up care
Active treatment with regular monitoring by a healthcare provider is recommended.
Calcium Channel Blockers
Vasodilator medications to manage headaches and potentially improve cerebral blood flow in Moyamoya patients.
Additional treatment options
Cerebral Angiography
Diagnostic catheter-based imaging to definitively assess vessel narrowing and collateral vessel formation patterns.
procedureCognitive and Behavioral Support
Neuropsychological assessment and counseling to address cognitive changes, anxiety, and depression associated with chronic cerebrovascular disease.
psychologicalHemodynamic Monitoring
Regular assessment of cerebral blood flow using techniques such as SPECT, PET, or acetazolamide challenge tests to evaluate vascular reserve.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Moyamoya Disease 5 C3279690?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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Compare medications used to treat Moyamoya Disease 5 C3279690. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy