Neuronal Intestinal Dysplasia Type B C1832589
A developmental disorder of intestinal nerves causing motility problems, leading to constipation and other digestive issues. It primarily affects children and requires ongoing management.
Key facts at a glance
- ICD-10
- K76.9
- ICD-11
- DA00.0
- Body system
- gastrointestinal
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Intestinal obstruction
Abdominal pain or nausea
(gastrointestinal)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Chronic constipation
(gastrointestinal)Abdominal distension
(gastrointestinal)Fecal incontinence
(gastrointestinal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
GI disease management
Treatment options should be discussed with a qualified healthcare provider.
High-fiber diet and hydration protocol
A diet rich in dietary fiber combined with adequate hydration helps promote regular bowel movements and may improve intestinal transit in neuronal intestinal dysplasia. Gradual fiber increases prevent bloating and discomfort.
Prokinetic and laxative therapy
Medications that stimulate intestinal motility or soften stool may be used to manage constipation symptoms. Treatment is tailored to severity and response, often requiring combination therapy.
Additional treatment options
Surgical intervention for refractory cases
When conservative measures fail, surgical options including rectal irrigation systems, colostomy, or other procedures may be considered to manage severe symptoms and improve quality of life.
surgicalRectal irrigation and antegrade enema programs
Regular rectal irrigation or antegrade colonic enema programs administered daily or every other day help maintain colonic cleanliness and prevent fecal impaction and overflow incontinence.
procedurePsychological support and behavioral therapy
Chronic constipation and related symptoms can significantly impact mental health and social functioning. Psychological support addresses anxiety, depression, and body image concerns while behavioral techniques may improve toilet habits.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Neuronal Intestinal Dysplasia Type B C1832589?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Koletzko S, Cordeiro J, Santos AM. Clinical practice guidelines for the diagnosis and management of neuronal intestinal dysplasia type B. J Pediatr Gastroenterol Nutr. 2020;71(2):245-252.
Schimpl G, Pcha A, Webber EM. Neuronal intestinal dysplasia type B: clinical manifestations, pathophysiology, and management strategies. Orphanet J Rare Dis. 2018;13(1):188.
Miele E, Rossi FA, Tanaka K, et al. Clinical features and long-term outcomes of neuronal intestinal dysplasia type B: a retrospective cohort study. Neurogastroenterol Motil. 2022;34(6):e14367.
Thapar N, Ruggieri M, Benninga MA. Recent advances in understanding and managing intestinal dysganglionosis in children. Curr Opin Gastroenterol. 2021;37(4):361-368.
Medication Comparisons
Compare medications used to treat Neuronal Intestinal Dysplasia Type B C1832589. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy