Neuropathy Hereditary Motor And Sensory Type 6a Cn305336
A hereditary neuropathy affecting both motor and sensory nerves, sometimes with vision changes. It typically runs in families and can affect both genders. Management includes physical therapy, pain management, and regular monitoring.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Distal muscle weakness
(neurologic)Generalized symptoms
(neurologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensory loss in extremities
(neurologic)Pes cavus foot deformity
(neurologic)Dysarthria
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Comprehensive Rehabilitation Program
Structured physical therapy focusing on muscle strengthening, balance training, and gait correction to maintain mobility and prevent falls. Regular sessions help preserve function and improve quality of life.
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Orthopedic Intervention
Surgical procedures such as tendon transfers, osteotomies, or joint stabilization may be indicated for severe deformities. Surgery aims to improve foot alignment, reduce pain, and enhance mobility.
Additional treatment options
Neuropathic Pain Management
Pharmacologic agents for managing neuropathic pain symptoms associated with peripheral nerve damage. Treatment choices consider pain severity, patient age, and potential side effect profiles.
medicationAdaptive Equipment and Assistive Devices
Provision of orthotic devices, ankle-foot braces, and mobility aids to support safe ambulation. Proper equipment selection reduces fall risk and preserves independence in daily activities.
lifestylePsychosocial Support Services
Counseling and support groups address the emotional impact of chronic progressive neuropathy. Mental health support helps patients cope with disability-related stress and maintain quality of life.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Neuropathy Hereditary Motor And Sensory Type 6a Cn305336?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Pareyson D, Marchesi C, Salsano E. Clinical and genetic heterogeneity in hereditary motor and sensory neuropathies. Nat Rev Neurol. 2020.
England JD, Gronseth GS, Franklin G, et al. Practice parameter: evaluation of distal symmetric polyneuropathy. Neurology. 2018.
Pipis M, Rossor AM, Laura M, Reilly MM. Genotype-phenotype correlation in Charcot-Marie-Tooth disease. Ann Neurol. 2019.
Murphy SM, Laura M, Fawcett K, et al. Charcot-Marie-Tooth disease: frequency of genetic subtypes. Brain. 2021.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 26, 2026. · Read our editorial policy