Neuropathy Hereditary Sensory And Autonomic Type 1a C5235211
A genetic disorder damaging sensory nerves, causing loss of feeling, pain, and ulcers. Typically inherited and progressive, requiring wound care and infection prevention.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Sudden severe neuropathic pain
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Loss of sensation in distal extremities
(neurologic)Distal muscle weakness
(neurologic)Recurrent foot ulcers
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Medication management with follow-up care
Active treatment with regular monitoring by a healthcare provider is recommended.
Sensory-Motor Rehabilitation
Targeted physical therapy addressing both sensory deficits and motor weakness characteristic of HSAN1A, focusing on balance training, proprioception exercises, and fall prevention strategies.
Pain and Symptom Pharmacological Management
Systematic medication management for neuropathic pain and associated symptoms including burning paresthesias, shooting pains, and autonomic manifestations of HSAN1A.
Additional treatment options
Injury Prevention and Skin Care Program
Comprehensive education and practical measures for preventing injuries and complications from sensory loss, including daily foot inspections, proper footwear selection, and wound care protocols.
lifestyleComprehensive Neurological Monitoring
Regular neurological assessments, nerve conduction studies, and autonomic function testing to track disease progression and inform treatment adjustments.
monitoringChronic Pain Psychological Support
Specialized psychological interventions including cognitive-behavioral therapy, acceptance and commitment therapy, and pain coping skills training for managing chronic neuropathic pain.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Neuropathy Hereditary Sensory And Autonomic Type 1a C5235211?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy