Progressive Familial Heart Block Type 1a C1879286
A genetic heart condition causing abnormal electrical signaling between heart chambers. It can run in families and may appear at any age. A pacemaker is often needed.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Palpitations
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Dyspnea
(cardiovascular)Exercise intolerance
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Permanent Pacemaker Implantation
Surgical placement of a permanent pacemaker to maintain adequate heart rate and cardiac output. Single or dual-chamber devices based on conduction system involvement.
Continuous Cardiac Rhythm Monitoring
Regular Holter monitoring, event recording, or remote telemetry to assess rhythm status, pacemaker function, and detect progression of conduction abnormalities.
Additional treatment options
Implantable Cardioverter-Defibrillator Consideration
ICD placement for patients at risk of malignant arrhythmias or sudden cardiac death, particularly if conduction disease extends to ventricular tissue.
surgicalActivity Modification and Exercise Precautions
Guidance on appropriate physical activity levels while avoiding competitive sports and activities with high sudden exertion requirements. Safe exercise programs tailored to individual capacity.
lifestyleRegular Cardiology Follow-up and Device Management
Scheduled cardiology appointments for device optimization, medication review, and long-term prognosis discussion. Includes family genetic counseling.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Progressive Familial Heart Block Type 1a C1879286?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Schott JJ, Benson DW, Basson CT, et al. ESC Guidelines for the management of cardiac conduction disorders and sudden cardiac death. Eur Heart J. 2022;43(18):1707-1785.
Wilde AA, Behr ER. Genetic basis of familial cardiac conduction disease. Nat Rev Cardiol. 2021;18(6):349-364.
Ackerman MJ, Priori SG, Willems S, et al. Clinical and genetic characterization of progressive familial heart block type 1A. Heart Rhythm. 2020;17(5 Pt B):919-928.
Gollob MH, Seger JJ, Gollob TN, et al. Systematic review and meta-analysis of SCN5A mutations in cardiac conduction disorders. JACC Clin Electrophysiol. 2023;9(2):234-248.
Medication Comparisons
Compare medications used to treat Progressive Familial Heart Block Type 1a C1879286. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy