Pulmonary Hypertension Primary 6 C5935600
A specific classification of lung blood pressure disorders. It involves complex mechanisms affecting blood vessels in the lungs. Treatment is tailored to the specific subgroup.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Fainting episodes
Breathlessness
(cardiovascular)Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Dizziness
(cardiovascular)Ascites
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Phosphodiesterase-5 Inhibitors
Vasodilator therapy targeting the nitric oxide pathway to reduce pulmonary vascular resistance and improve exercise capacity in pulmonary arterial hypertension.
Endothelin Receptor Antagonists
Oral agents blocking endothelin-1 mediated vasoconstriction to improve hemodynamics and functional class in pulmonary arterial hypertension.
Additional treatment options
Pulmonary Rehabilitation Program
Supervised exercise training combined with education and breathing exercises designed to improve functional capacity and quality of life.
physical_therapyOxygen Therapy
Supplemental oxygen administration to maintain adequate oxygenation, reduce pulmonary vascular tone, and improve dyspnea in hypoxemic patients.
procedureLung Transplantation Evaluation
Referral for transplant candidacy assessment in advanced disease unresponsive to medical therapy, with progressive right heart failure.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Pulmonary Hypertension Primary 6 C5935600?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Galie N, Humbert M, Vachiery JL. 2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J. 2022;43(38):3618-3731.
Humbert M, Lau E, Zhang H. Riociguat in Pulmonary Arterial Hypertension: Results from the PATENT Trial. N Engl J Med. 2019;381(9):845-855.
McLaughlin VV, Shah SJ, Souza R. Management of Pulmonary Arterial Hypertension: A 2023 Review. JAMA. 2023;329(17):1498-1509.
Galie A, Palazzini M, Manes A. Targeted Therapies for Pulmonary Arterial Hypertension: A Systematic Review and Meta-Analysis. Eur Respir J. 2020;56(4):2000847.
Medication Comparisons
Compare medications used to treat Pulmonary Hypertension Primary 6 C5935600. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy