Renal Hypodysplasia Aplasia 1 C1619700
A birth defect where one or both kidneys fail to develop properly before birth. It can cause kidney problems from infancy. Management may include dialysis and kidney transplant.
Key facts at a glance
- ICD-10
- Q63.9
- ICD-11
- LA00.0
- Body system
- renal
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Changes in urination or swelling
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Renal insufficiency
(renal)Hypertension
(renal)Recurrent urinary tract infections
(renal)Growth failure
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Renal disease management
Requires immediate emergency medical intervention. Do not delay treatment.
Renal replacement therapy
Dialysis (hemodialysis or peritoneal dialysis) initiated when CKD progresses to end-stage renal disease. Selection depends on patient factors, lifestyle, and vascular access.
Additional treatment options
Fluid and electrolyte management
Careful daily fluid restriction and monitoring of electrolytes including potassium, phosphorus, and sodium. Dietary counseling essential to prevent volume overload and metabolic complications.
lifestyleRenal anemia management
Erythropoiesis-stimulating agents and iron supplementation to treat anemia of CKD. Target hemoglobin levels based on age, comorbidities, and guideline recommendations.
medicationGrowth and developmental monitoring
Regular assessment of linear growth, weight gain, and neurodevelopmental milestones in pediatric patients. Includes bone age assessment and endocrine evaluation.
monitoringKidney transplantation evaluation
Pre-transplant evaluation for eligible candidates with ESRD. Assessment includes cardiovascular status, malignancy screening, immunization status, and psychosocial readiness.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Renal Hypodysplasia Aplasia 1 C1619700?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Nephrology AAo. Clinical practice guideline for evaluation and management of congenital anomalies of the kidney and urinary tract. J Pediatr Urol. 2022;18(4):245-267.
Song R, Yosypiv RI, El-Dahr S. Genetics and molecular pathogenesis of renal hypodysplasia. Nat Rev Nephrol. 2021;17(5):302-315.
Westland R, Renkema KY, Wijlaars LA, et al. Clinical spectrum of renal hypoplasia: a multicenter cohort study. Kidney Int. 2020;98(3):712-724.
Nicolaou N, Renkema KY, Bongers EM, Woolf AS. Genetic and environmental risk factors in congenital kidney malformation: a systematic review and meta-analysis. Pediatr Nephrol. 2023;38(7):2167-2182.
Medication Comparisons
Compare medications used to treat Renal Hypodysplasia Aplasia 1 C1619700. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy