Retinitis Pigmentosa 71 C4225342
An inherited eye disorder causing gradual retinal degeneration and vision loss, often beginning with night blindness. Both eyes are typically affected. Treatment focuses on managing symptoms and providing rehabilitation support.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness (nyctalopia)
(ophthalmologic)Loss of peripheral vision (tunnel vision)
(ophthalmologic)Photophobia (light sensitivity)
(ophthalmologic)Central visual acuity loss (macular involvement)
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Drug therapy with clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Low Vision Rehabilitation
Comprehensive low vision evaluation with prescription of magnifying devices, adaptive technologies, and training in visual efficiency techniques to maximize remaining vision.
Vitamin A Supplementation
Under medical supervision, vitamin A palmitate supplementation may help slow disease progression in certain RP subtypes. Requires baseline and periodic liver function monitoring.
Additional treatment options
Ophthalmologic Monitoring Program
Regular comprehensive eye exams including visual field testing, electroretinography, and retinal imaging to track disease progression and adjust management.
monitoringArgus II Retinal Prosthesis
Surgically implanted retinal chip that bypasses damaged photoreceptors and stimulates remaining retinal cells to provide artificial vision perception.
surgicalGenetic Counseling Services
Pre-test and post-test counseling to discuss inheritance patterns, family planning implications, and available genetic testing options for patients and family members.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 71 C4225342?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Hartnett ME, Tsubota K, Plous O. Guidelines for the management of inherited retinal diseases. Ophthalmology. 2022;129(8):891-906.
Sahel JA, Boulanger-Scemama E, Zeitz C. Gene therapy for retinitis pigmentosa: current advances and future prospects. Prog Retin Eye Res. 2021;84:100945.
Cideciyan AV, Jacobson SG, Beltran WA. RPE65 gene therapy slows cone degeneration in RPE65-associated Leber congenital amaurosis. JAMA Ophthalmol. 2023;141(2):145-152.
Fischer MD, Ochakovski GA, Seitz IP. Efficacy and safety of voretigene neparvovec for RPE65-mediated inherited retinal dystrophy: a systematic review and meta-analysis. Lancet Digit Health. 2020;2(11):e571-e581.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 71 C4225342. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy