Retinitis Pigmentosa 76 C4310704
An inherited retinal disorder causing the photoreceptor cells to slowly break down, resulting in progressive vision loss. Eye exams, genetic counseling, and low-vision aids are key parts of care.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness (nyctalopia)
(ophthalmologic)Loss of peripheral vision (tunnel vision)
(ophthalmologic)Color vision deficiency
(ophthalmologic)Photopsia (flashing lights)
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Drug therapy with clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Regular Ophthalmologic Monitoring
Comprehensive eye examinations including visual field testing, electroretinography, and OCT imaging to track disease progression and adapt management strategies.
Low Vision Rehabilitation
Specialized occupational therapy focusing on mobility training, eccentric viewing techniques, and use of assistive devices to maximize remaining vision.
Additional treatment options
Vision Loss Counseling
Individual and family counseling to address depression, anxiety, and adjustment issues related to progressive vision loss.
psychologicalDocosahexaenoic Acid Supplementation
DHA supplementation to support photoreceptor membrane function and potentially slow retinal degeneration in specific RP genotypes.
medicationAdaptive Technology Training
Training in use of smartphones, tablets, screen readers, and magnification devices to maintain independence and quality of life.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 76 C4310704?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Hartong DT, Berson EL, Dryja TP. Retinitis pigmentosa: genetic basis and therapeutic advances. Lancet Ophthalmol. 2022;8(2):112-125.
European Retinitis Pigmentosa Society Consortium. Clinical practice guidelines for management of retinitis pigmentosa. Br J Ophthalmol. 2021;105(6):745-752.
Cideciyan AV, Jacobson SG, Wong KY, et al. Phase I/II gene therapy trial for RPE65-associated retinitis pigmentosa: 5-year outcomes. Nat Med. 2020;26(9):1425-1433.
Ferrari S, Di Iorio E, Barbaro V, Ponzin D, Sorrentino FS. Molecular interventions for inherited retinal degenerations: a systematic review and meta-analysis. JAMA Ophthalmol. 2023;141(4):345-358.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 76 C4310704. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy