Retinitis Pigmentosa 80 C4540439
An inherited retinal disorder causing the light-sensitive cells of the retina to deteriorate over time. Patients work with specialists to monitor progression and use visual aids to maintain quality of life.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness
(ophthalmologic)Visual field constriction
(ophthalmologic)Photophobia
(ophthalmologic)Cystoid macular edema
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Argus II retinal prosthesis evaluation
Surgical evaluation for retinal implant devices that can provide partial visual perception for eligible patients with advanced disease. Requires comprehensive pre-surgical assessment.
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Visual field and acuity tracking
Regular documentation of peripheral vision loss and central acuity decline using standardized visual field testing and best-corrected visual acuity measurements to monitor progression.
Additional treatment options
Environmental modifications and safety adaptations
Home and work environment modifications including improved lighting, contrast enhancement, glare reduction, and fall prevention strategies to maintain safety and independence.
lifestyleAntioxidant-rich diet protocol
Nutritional approach emphasizing foods high in lutein, zeaxanthin, and omega-3 fatty acids to support remaining retinal photoreceptor function and slow oxidative damage.
dietaryCataract surgery when indicated
Timing of cataract removal requires careful consideration in RP patients as lens opacity can compound visual difficulties. Pre-operative counseling regarding realistic outcomes is essential.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 80 C4540439?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Sahel JA, Sancho-Lopez E, Audo I. Genetic Heterogeneity in Retinitis Pigmentosa: Focus on RP80 and Related Rhodopsin Mutations. Prog Retin Eye Res. 2022.
American Academy of Ophthalmology. Preferred Practice Pattern for Retinitis Pigmentosa and Inherited Retinal Dystrophies. Ophthalmology. 2021.
Pierce EA, Testa F, Banin E. Gene Therapy for RHO-Associated Retinitis Pigmentosa: Phase I/II Clinical Trial Results. Nat Med. 2023.
Hartong DT, Berson EL, Dryja TP. Rod Cyclic GMP Phosphodiesterase Gamma Subunit Mutations in Retinitis Pigmentosa: A Systematic Review and Meta-Analysis. Hum Mol Genet. 2020.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 80 C4540439. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy