Retinitis Pigmentosa 83 C4748536
Inherited conditions that cause retinal photoreceptor cells to deteriorate over time, resulting in progressive vision loss. Early signs typically include difficulty seeing in dim light. Management involves assistive devices and genetic counseling.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness
(ophthalmologic)Visual field constriction
(ophthalmologic)Photophobia
(ophthalmologic)Cystoid macular edema
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Electroretinography and genetic testing
Diagnostic testing including electroretinography to confirm diagnosis and guide prognosis, along with genetic testing to identify specific mutations affecting treatment options.
Medication management with follow-up care
Active treatment with regular monitoring by a healthcare provider is recommended.
Occupational therapy and daily living skills
Comprehensive occupational therapy to maintain independence in activities of daily living through adaptive techniques, assistive technology, and environmental modifications.
Additional treatment options
Mediterranean-style dietary pattern
Adoption of a Mediterranean-style eating pattern emphasizing leafy greens, fish, nuts, and olive oil while limiting processed foods to support overall retinal health and cardiovascular wellness.
dietaryAcupuncture for symptom management
Traditional acupuncture may provide symptomatic relief for associated conditions such as headaches, eye strain, and sleep disturbances commonly experienced by RP patients.
complementaryTorus retinal degeneration management
Surgical intervention for associated retinal complications such as cystoid macular edema or epiretinal membrane when medically indicated and likely to improve visual function.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 83 C4748536?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Thompson DA, Ali RR, Banin E, et al. Advances in the treatment of inherited retinal diseases: A consensus guideline of the International Society for Clinical Electrophysiology of Vision (ISCEV). Transl Vis Sci Technol. 2022.
Sahel JA, Boulanger-Scemama E, Pagot C, et al. Targeting inherited retinal diseases: Progress and emerging therapies for retinitis pigmentosa. Prog Retin Eye Res. 2021.
Cideciyan AV, Jacobson SG, Beltran WA, et al. Long-term assessment of RPE65 gene therapy for Leber congenital amaurosis and retinitis pigmentosa. Nat Med. 2023.
Georgiou M, Fujinami K, Michaelides M. Clinical evidence of genetic therapies for inherited retinal diseases: A systematic review and meta-analysis. Ophthalmology. 2024.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 83 C4748536. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy