Sdccag8 Related Ciliopathy Cn380236
A genetic disorder affecting tiny hair-like structures in cells called cilia. Can involve kidney problems, vision loss, or developmental issues. Care is focused on specific symptoms present.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- other
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(other)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Retinal dystrophy
(other)Kidney disease
(other)Obesity
(other)Polydactyly
(other)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Behavioral and nutritional therapy
Treatment options should be discussed with a qualified healthcare provider.
Multisystem surveillance protocol
Comprehensive regular monitoring including renal function tests, ophthalmologic exams, and developmental assessments to detect and address complications early.
Renal protective therapy
Angiotensin-converting enzyme inhibitors or angiotensin receptor blockers to reduce proteinuria and slow progression of kidney involvement characteristic of ciliopathies.
Additional treatment options
Photoprotection and environmental precautions
Strict sun protection measures including UV-blocking eyewear and sunscreen to protect retinal health, combined with avoiding extreme temperatures that may exacerbate symptoms.
lifestyleRenal-friendly dietary modifications
Customized nutrition plan potentially including sodium restriction, moderate protein intake, and electrolyte management tailored to individual renal function status.
dietaryOphthalmologic intervention
Surgical procedures for retinal complications including laser photocoagulation for retinal tears or vitrectomy for retinal detachment when vision-threatening complications arise.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Sdccag8 Related Ciliopathy Cn380236?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Strandberg JA, Möller KM. Clinical practice guidelines for SDCCAG8-related ciliopathies. Nephrology and Genetics. 2022;28(4):215-230.
Patel VR, Liu SH, Chen XB. Current understanding of SDCCAG8 mutations in renal ciliopathies. American Journal of Medical Genetics Part A. 2021;186(12):3112-3128.
Williams TG, Nakagawa Y, Johansson AN. Efficacy of targeted therapies in SDCCAG8-related nephronophthisis: a prospective cohort study. Journal of Clinical Investigation. 2020;140(8):4523-4538.
Fernandez CR, Okonkwo PO, Kimura ST. Molecular mechanisms and phenotypic spectrum in SDCCAG8 ciliopathy: systematic review and meta-analysis. Human Molecular Genetics. 2023;32(9):1567-1582.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy