Type I Truncus Arteriosus C1834934
A congenital heart defect where one large vessel carries blood from the heart. Newborns require surgical repair to restore normal blood flow.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Central cyanosis
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Respiratory distress
Failure to thrive
(cardiovascular)Digital clubbing
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complete truncus arteriosus repair
Open heart surgery to separate pulmonary arteries from the truncus, close the ventricular septal defect, and establish right ventricular to pulmonary artery continuity using a conduit.
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Prostaglandin E1 infusion
Continuous intravenous infusion to maintain ductal patency pre-operatively, ensuring adequate pulmonary blood flow until surgical correction can be performed.
Additional treatment options
Pulmonary hypertension management
Afterload reduction and pulmonary vasodilation therapy to manage elevated pulmonary vascular resistance common in truncus arteriosus.
medicationLong-term cardiac surveillance
Lifetime echocardiographic and clinical monitoring for conduit degeneration, truncal valve function, and ventricular performance with planned reintervention as needed.
monitoringCardiac catheterization for assessment
Diagnostic catheterization to evaluate pulmonary artery anatomy, vascular resistance, and truncal valve function prior to definitive surgical repair.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Type I Truncus Arteriosus C1834934?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease. Circulation. 2019.
Mair DD, Edwards WD, Julsrud PR. Truncus arteriosus. In: Allen HD, ed. Moss and Adams Heart Disease in Infants, Children, and Adolescents. 8th ed. Lippincott Williams & Wilkins; 2015.
Brown JW, Ruzmetov M, Okada T, et al. Truncus arteriosus repair: outcomes and risk factors. Ann Thorac Surg. 2021.
Crucean A, Brauer R, Hraska V, et al. Early outcomes of truncus arteriosus repair: a single-center experience. Eur J Cardiothorac Surg. 2017.
Medication Comparisons
Compare medications used to treat Type I Truncus Arteriosus C1834934. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy