Cysteamine Bitartrate
Procysbi is a brand-name delayed-release medication containing cysteamine bitartrate, designed to manage nephropathic cystinosis in adults and children. It helps reduce harmful cystine buildup in cells, which can otherwise damage organs including kidneys, eyes, and other tissues. This medication requires consistent, careful dosing on an empty stomach to be effective.
Procysbi is a specialty medication used to treat the rare genetic disorder nephropathic cystinosis by reducing cystine levels in the body.
Key facts at a glance
- RxNorm
- 1421468
- Generic
- Procysbi
- Class
- brand-name
- Brands
- —
- Availability
- rx
- Lactation
- unknown
- Routes
- —
- Forms
- —
- Regions
- US, EU, CN, JP
- Monitoring
- —
This page is for informational purposes only.
Do not use this information to diagnose yourself or to replace a physician's advice. Always consult a qualified healthcare provider before starting, stopping, or changing any medication. If you believe you are experiencing a medical emergency, call your local emergency number immediately.
Procysbi is indicated for the treatment of nephropathic cystinosis, a rare genetic lysosomal storage disorder characterized by accumulation of the amino acid cystine in various organs including kidneys, eyes, muscles, brain, and white blood cells.
Procysbi contains cysteamine, which converts to its active metabolite cysteamine and reacts with cystine to form cysteine and cysteine-cysteamine mixed disulfide, allowing for reduced cystine accumulation within cells.
Procysbi is a brand-name medication with no generic equivalent currently available. It must be taken on an empty stomach, at least 30 minutes before or 2 hours after food. Capsule contents may be sprinkled on certain foods. Patients should follow prescribed dosing schedules carefully and discuss potential side effects with their healthcare provider.
Official drug label
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This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 9, 2026. · Read our editorial policy