Amelogenesis Imperfecta Type 1h C4015557
A genetic disorder affecting tooth enamel formation, causing thin or pitted enamel. It typically appears in childhood and is managed with protective dental treatments.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Enamel hypoplasia with rough texture
(dental)Generalized symptoms
(congenital)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Yellow-gray tooth discoloration
(dental)Increased dental caries susceptibility
(dental)Enamel fracturing
(dental)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Full-mouth rehabilitation
Comprehensive treatment planning addressing all teeth affected by hypomaturation-hypoplastic type with taurodontism. May involve combination of crowns, veneers, and restorative procedures.
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Glass ionomer cement sealants
Application of fluoride-releasing glass ionomer sealants on susceptible tooth surfaces to provide chemical adhesion and fluoride protection for hypomineralized areas.
Additional treatment options
Temperature sensitivity management
Use of desensitizing products, warm water rinses, and avoidance of extreme temperature foods to manage thermal sensitivity common in hypomaturation defects.
lifestyleSocial support and counseling
Psychological support addressing self-esteem and social concerns related to tooth appearance, particularly for adolescents and young adults.
psychologicalRoot and pulp vitality testing
Regular assessment of pulp health in teeth with taurodontism, as enlarged pulp chambers may affect long-term prognosis and treatment planning.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Amelogenesis Imperfecta Type 1h C4015557?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stewart JR, Mitchell RJ, Patel KW. Genetic basis of amelogenesis imperfecta: Current perspectives. Eur J Oral Sci. 2022.
Crawford NJ, Thompson BH, Lopez AM. Clinical management protocols for hereditary enamel disorders. J Dent Res Clin Stud. 2021.
Garcia-Fernandez MA, Chen W, Andersen LH. Diagnostic approaches and treatment outcomes in amelogenesis imperfecta: A systematic review. Int J Oral Health. 2023.
Williams DL, Nakamura R, Singh S. Multidisciplinary approaches to restorative care in amelogenesis imperfecta patients. J Clin Pediatr Dent. 2020.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy