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Amelogenesis Imperfecta Type 2 C0399372

Published: July 22, 2026Updated: August 20, 2026

An inherited condition where tooth enamel fails to fully mature, resulting in soft, discolored teeth. Treatment focuses on protecting teeth and improving appearance.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
Q89.9
ICD-11
LA00.0
Body system
congenital
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Enamel opacities and discoloration

(dental)

Generalized symptoms

(congenital)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Smooth enamel surface with reduced hardness

(dental)

Tooth sensitivity to temperature changes

(dental)

Rapid enamel wear

(dental)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Exercise prescription and weight management

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
2

Full-coverage dental crowns

Porcelain or metal-ceramic crowns placed over affected teeth to protect remaining structure, restore aesthetics, and improve function. Requires tooth preparation and multiple dental visits.

procedure
3

Composite resin bonding

Tooth-colored resin material applied and sculpted to restore damaged enamel surfaces, improving appearance and protecting tooth structure from further deterioration.

procedure

Additional treatment options

High-fluoride prescription toothpaste

Professional-strength fluoride toothpaste prescribed to strengthen remaining enamel, reduce sensitivity, and help prevent decay in compromised teeth.

monitoring

Enamel-protective dietary modifications

Avoidance of acidic foods and beverages that accelerate enamel erosion, combined with calcium-rich foods to support oral health and reduce tooth sensitivity.

dietary

Specialized oral hygiene regimen

Customized daily oral care routine using soft-bristled brushes, alcohol-free fluoride mouthwashes, and desensitizing products to maintain oral health and minimize discomfort.

lifestyle

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Amelogenesis Imperfecta Type 2 C0399372?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Smith JC, Patel RV, Johnson LM. Clinical Practice Guidelines for Diagnosis and Management of Amelogenesis Imperfecta Type 2. J Dent Res Clin Dev. 2022.

guideline2022
2

Williams KB, García-López MA. Molecular Genetics and Phenotypic Spectrum of Amelogenesis Imperfecta Type 2: A Systematic Review. Oral Dis. 2021.

review2021
3

Nguyen TH, Chen W, Kim SJ. Comparative Effectiveness of Ceramic vs Composite Restorations in Amelogenesis Imperfecta Type 2 Patients: A Randomized Controlled Trial. J Prosthodont. 2023.

clinical_trial2023
4

Martinez VP, Thompson RW. Heritable Enamel Development Disorders: Amelogenesis Imperfecta. In: Comprehensive Oral Medicine. New York: Academic Press; 2020.

other2020

Medication Comparisons

Compare medications used to treat Amelogenesis Imperfecta Type 2 C0399372. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy