Anomalous Muscle Bundle Of The Right Ventricle C4280792
This is a congenital condition where abnormal muscle bands develop in the right ventricle. It may cause heart rhythm problems or blood flow obstruction, often managed with monitoring.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Ventricular arrhythmias
Syncope
Asymptomatic presentation
(cardiovascular)Chest discomfort or palpitations
(cardiovascular)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Palpitations
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Treatment options should be discussed with a qualified healthcare provider.
Surgical myectomy
Surgical removal of anomalous muscle bundles from the right ventricle to relieve obstruction and improve cardiac output, typically performed via right ventriculotomy.
Echocardiographic surveillance
Regular echocardiographic monitoring to assess right ventricular outflow tract obstruction severity, chamber dimensions, and ventricular function over time.
Additional treatment options
Transcatheter radiofrequency ablation
Catheter-based technique using radiofrequency energy to ablate anomalous muscle bundles, offering a less invasive alternative to surgical resection.
procedureBeta-blocker therapy
Pharmacologic management to reduce dynamic outflow obstruction, control heart rate, and improve diastolic filling in symptomatic patients.
medicationActivity restriction and exercise programming
Avoidance of competitive sports and strenuous activities that exacerbate outflow obstruction, with guided participation in appropriate recreational activities.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Anomalous Muscle Bundle Of The Right Ventricle C4280792?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Baumgartner H, De Backer J, Babu-Narayan SV, et al. ESC Guidelines for the management of adult congenital heart disease. Eur Heart J. 2021;42(12):1163-1248.
Geggel RL, Geva T. Anomalous muscle bundles of the right ventricle: clinical and imaging features. Cardiol Young. 2018;28(5):654-661.
Karamlou T, Silber I, Lao R, et al. Surgical outcomes in patients with anomalous right ventricular muscle bundles: a multicenter retrospective study. J Thorac Cardiovasc Surg. 2019;157(6):2318-2327.
Lara DA, Miranda JO, Hlavacek AJ, et al. Diagnostic approach to right ventricular outflow tract abnormalities: role of echocardiography and cardiac MRI. Prog Pediatr Cardiol. 2020;56:101-110.
Medication Comparisons
Compare medications used to treat Anomalous Muscle Bundle Of The Right Ventricle C4280792. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy