Anomalous Origin Of Coronary Artery From The Pulmonary Artery C4023252
A condition where the coronary arteries connect to the pulmonary artery instead of the aorta, affecting blood flow to the heart muscle. It primarily affects infants with congenital heart defects and typically requires surgical correction to restore normal blood flow.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Chest pain
Syncope
Dyspnea
(cardiovascular)Failure to thrive
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Coronary artery reimplantation to aorta
Direct surgical reimplantation of the anomalous coronary artery from the pulmonary artery back to the aortic root provides definitive anatomical correction and restores dual coronary circulation.
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Coronary artery bypass grafting
Creation of a bypass from the aorta to the affected coronary artery using saphenous vein or internal mammary artery graft provides alternative blood supply to the myocardium.
Additional treatment options
Beta-blocker therapy for symptom control
Beta-blockers reduce myocardial oxygen demand and help manage symptoms of myocardial ischemia in patients awaiting surgical repair or who are not surgical candidates.
medicationLong-term cardiac surveillance program
Regular echocardiography, stress testing, and cardiac MRI monitoring detects late complications including coronary stenosis at anastomotic sites, ventricular dysfunction, and mitral regurgitation.
monitoringActivity modification and exercise guidance
Structured guidance on physical activity limitations prevents excessive cardiac stress while maintaining cardiovascular fitness. Competitive sports restriction often recommended pending surgical repair and reassessment.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Anomalous Origin Of Coronary Artery From The Pulmonary Artery C4023252?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Warnes CA, Williams RG, Bashore TM, et al. ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease. J Am Coll Cardiol. 2008.
Schicchi N, Secchi F, Sturini M, et al. Anomalous origin of coronary artery from pulmonary artery: a review. Radiol Med. 2021.
Padalino MA, Fortunato W, Stellin G, et al. Surgical repair of anomalous coronary artery from pulmonary artery: a 20-year experience. Ann Thorac Surg. 2019.
Gaurav A, Taksande A, Shelke V. ALCAPA syndrome: pathophysiology and management. Curr Cardiol Rev. 2022.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy