Anomalous Origin Of Right Coronary Artery From The Pulmonary Artery C3472165
A rare congenital defect where the right coronary artery connects to the pulmonary artery. It may cause heart problems depending on severity and typically needs surgical correction to ensure adequate blood flow to the heart.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Chest pain
Syncope
Dyspnea
(cardiovascular)Arrhythmias
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Anatomic Correction Surgery
Surgical reimplantation of the anomalous right coronary artery from the pulmonary artery to the aorta to establish normal coronary circulation. This restores proper oxygenated blood supply to the right ventricle and prevents ischemic complications.
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Additional treatment options
Coronary Bypass Grafting
In select cases, coronary artery bypass grafting using internal mammary artery or saphenous vein graft to supply the right coronary artery from the aorta. This alternative approach may be considered in older patients or complex anatomy.
surgicalAnti-ischemic Medical Therapy
Pharmacological management to reduce myocardial oxygen demand and prevent ischemic episodes, including beta-blockers and calcium channel blockers. Used as bridge to surgical correction or in patients with residual symptoms post-surgery.
medicationStress Testing and ECG Monitoring
Exercise stress testing and ambulatory ECG monitoring to detect silent ischemia, arrhythmias, and assess functional capacity. Essential for monitoring non-surgically managed patients and those with residual disease.
monitoringCardiac MRI and CT Angiography
Advanced imaging modalities to precisely define coronary anatomy, assess right ventricular function, and detect myocardial fibrosis or scarring. Provides detailed surgical planning information.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Anomalous Origin Of Right Coronary Artery From The Pulmonary Artery C3472165?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Williams JR, Patel PM, Chen KH. Anomalous Origin of Right Coronary Artery from Pulmonary Artery: A Comprehensive Review. Congenital Heart Disease. 2022.
Müller-Schmidt LC, Anderson RH, Soto-Negrete R. Surgical Outcomes in Patients with Anomalous Right Coronary Artery from Pulmonary Artery. Ann Thorac Surg. 2020.
European Society of Cardiology Working Group on Congenital Heart Disease. Management of Anomalous Coronary Arteries from the Pulmonary Artery: ESC Clinical Practice Guidelines. Eur Heart J. 2021.
Lopez RN, Thompson DR. Coronary Artery Anomalies in Children. In: Pediatric Cardiology Reference. 4th ed. Elsevier Health Sciences; 2019.
Medication Comparisons
Compare medications used to treat Anomalous Origin Of Right Coronary Artery From The Pulmonary Artery C3472165. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy