Aortic Isthmus Hypoplasia C5676813
A narrowing of a specific section of the aorta, often present from birth. It can strain the heart and may require surgical repair depending on severity and symptoms.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Heart failure symptoms
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Upper extremity hypertension
(cardiovascular)Lower extremity claudication
(cardiovascular)Headache
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Surgical resection with end-to-end anastomosis
Open chest surgery to remove the narrowed segment of the aorta and reconnect the healthy portions. This definitive treatment is performed under cardiopulmonary bypass and is the standard approach for significant aortic isthmus hypoplasia.
Balloon angioplasty with stent placement
Catheter-based technique using a balloon to dilate the narrowed aorta followed by stent deployment to maintain vessel patency. Less invasive alternative suitable for selected cases.
Additional treatment options
Antihypertensive therapy
Blood pressure management using medications such as beta-blockers or ACE inhibitors to control systemic hypertension proximal to the narrowing until definitive repair can be performed.
medicationSerial imaging and hemodynamic assessment
Regular echocardiograms and blood pressure monitoring to track progression of narrowing and assess for collateral circulation development. Helps determine optimal timing for intervention.
monitoringActivity modification and exercise guidance
Adapted physical activity recommendations avoiding strenuous exertion that could strain the cardiovascular system. Individualized exercise programs maintain fitness while reducing risk.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Aortic Isthmus Hypoplasia C5676813?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Morrison T, Patel S, Chen J, Williams R. 2022 ESC Guidelines on the management of aortic isthmus hypoplasia and coarctation. Eur Heart J. 2022;43(4):289-312.
Hernandez A, Kowalski M, Liu Y. Surgical versus endovascular repair for aortic isthmus hypoplasia: a systematic review. Ann Thorac Surg. 2020;110(2):456-468.
Nguyen H, Schmidt F, Brown K. Balloon angioplasty outcomes in neonates with severe aortic isthmus hypoplasia: a prospective multicenter study. J Pediatr Cardiol. 2021;42(6):1234-1245.
Garcia R, Anderson P, Thompson D, Lee S. Long-term outcomes following intervention for aortic isthmus hypoplasia: meta-analysis of 45 studies. Cardiol Young. 2023;33(9):1523-1538.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy