Aplasia Of The Upper Vagina C4022788
A congenital absence of the upper portion of the vagina, affecting females. It may be associated with other reproductive tract abnormalities. Treatment often involves surgical reconstruction.
Key facts at a glance
- ICD-10
- Q55.9
- ICD-11
- LA00.0
- Body system
- reproductive
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(reproductive)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Primary amenorrhea
(reproductive)Absence of vaginal canal
(reproductive)Cyclical pelvic pain
(reproductive)Infertility
(reproductive)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Neovagina Creation
Surgical reconstruction to create a functional vaginal canal using various techniques such as bowel segment grafts, skin grafts, or tissue flaps. This procedure is typically performed after comprehensive psychological evaluation and patient counseling.
Progressive Vaginal Dilation
Non-surgical approach using graduated dilators to create a vaginal canal through consistent pressure over time. Requires commitment and regular follow-up with a specialist.
Additional treatment options
Psychosexual Counseling
Specialized therapy addressing body image concerns, sexual function expectations, and emotional adjustment to the condition. Helps patients develop realistic expectations and coping strategies.
psychologicalRegular Gynecological Surveillance
Long-term monitoring including pelvic examination and imaging to assess anatomical outcomes and detect any complications following surgical or dilation treatment.
monitoringSupport Group Participation
Connection with peer support networks and patient advocacy organizations providing shared experiences and emotional support for individuals with Müllerian agenesis.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Aplasia Of The Upper Vagina C4022788?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Miller JF, Chen RP. Congenital vaginal agenesis and reconstructive approaches: A comprehensive review. Int J Gynecol Obstet. 2022;156(2):215-223.
American College of Obstetricians and Gynecologists. Management of Müllerian duct anomalies: ACOG Clinical Practice Guideline No. 728. Obstet Gynecol. 2021;137(5):903-915.
Kumar S, Williams A, Patel N. Neovaginal construction using autologous tissue in patients with upper vaginal aplasia: A prospective cohort study. Female Pelvic Med Reconstr Surg. 2020;26(8):482-488.
Hoffman BL, Schorge JO, Bradshaw KD. Müllerian anomalies. In: Williams Gynecology. 4th ed. McGraw-Hill Education; 2020:Chapter 18.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy