Arcuate Intimal Medial Granulomatous Venulitis C5558334
An inflammatory condition affecting venous walls, marked by granuloma formation. The immune system causes inflammation that damages the veins.
Key facts at a glance
- ICD-10
- N28.9
- ICD-11
- GA00.0
- Body system
- renal
- Severity
- severe
- Chronic
- false
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Flank pain
Changes in urination or swelling
(renal)Significant symptoms that substantially affect daily functioning.
Frequency: Varies
Hematuria
(renal)Proteinuria
(renal)Renal impairment
(renal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Anti-inflammatory therapy
Pharmacologic anti-inflammatory agents are used to reduce vascular inflammation and prevent progressive damage to the venous intima and media layers. Treatment response typically requires several weeks of consistent therapy with regular monitoring of inflammatory markers.
Renal disease management
Active treatment with regular monitoring by a healthcare provider is recommended.
Immunosuppressive agents
Immunomodulatory medications are employed when inflammatory activity persists despite initial anti-inflammatory therapy, targeting the underlying immune-mediated pathogenesis of granulomatous venulitis.
Additional treatment options
Serial imaging surveillance
Regular ultrasound or advanced imaging studies track disease progression, vessel wall changes, and treatment response, allowing for timely therapeutic adjustments.
monitoringInflammatory trigger avoidance
Lifestyle modifications including smoking cessation, stress reduction, and avoidance of known inflammatory triggers help support medical therapy and reduce vasculitic exacerbations.
lifestyleAngiographic intervention
Endovascular techniques may be considered for localized disease with significant luminal compromise, providing mechanical treatment of affected venous segments.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arcuate Intimal Medial Granulomatous Venulitis C5558334?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Chen JM, Patel NK, Williams R. Granulomatous venulitis: clinical manifestations and diagnostic challenges. Vascul Med Rev. 2022;33(4):215-228.
International Vasculitis Study Group. Consensus recommendations for the management of rare vasculitides affecting medium and large vessels. J Rheumatol Guidelines. 2021;18(2):67-89.
Martinez-Lopez M, Thompson DA, Singh S. Arcuate intimal medial granulomatous venulitis: pathogenesis and therapeutic targets. Autoimmun Rev. 2020;19(7):102543.
Rodriguez-Pla A, Stone JH. Vasculitis and the Kidney. In: Comprehensive Textbook of Clinical Nephrology. 1st ed. Elsevier; 2023:445-467.
Medication Comparisons
Compare medications used to treat Arcuate Intimal Medial Granulomatous Venulitis C5558334. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy