Arrhythmogenic Right Ventricular Dysplasia 13 C3810138
A genetic heart condition where heart muscle is replaced by fatty tissue, mainly affecting the right ventricle and causing irregular heartbeats. It typically affects young adults and can run in families. Treatment includes medications, procedures, and implanted devices to manage arrhythmias and reduce sudden death risk.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Ventricular tachycardia
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Palpitations
(cardiovascular)Lightheadedness
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Antiarrhythmic Drug Therapy
Comprehensive pharmacologic management using beta-blockers as foundation therapy with addition of sotalol or dofetilide for refractory ventricular arrhythmias. Requires baseline and periodic QT interval monitoring.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Ventricular Tachycardia Ablation
Electrophysiology-guided ablation targeting VT circuits in the right ventricular outflow tract and other arrhythmogenic zones. May require multiple procedures for durable control given the progressive nature of ARVD13.
Additional treatment options
Activity Modification Program
Comprehensive exercise counseling and activity restriction program tailored to disease severity, focusing on avoiding competitive athletics and high-intensity sustained exercise that accelerates RV remodeling.
lifestyleStress Management
Psychological support and stress reduction techniques including mindfulness, relaxation training, and counseling to reduce arrhythmia triggers associated with emotional stress and anxiety.
complementaryHeart Transplantation Evaluation
Transplant candidacy assessment for patients with end-stage ARVD13 experiencing recurrent ICD storms, progressive heart failure despite optimal therapy, or inoperable ventricular arrhythmias.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Right Ventricular Dysplasia 13 C3810138?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the task force criteria. J Am Coll Cardiol. 2010.
Corrado D, Basso C, Judge DP. Arrhythmogenic right ventricular cardiomyopathy. Nat Rev Dis Primers. 2021.
Calkins H, Zipes DP, Bilchick KC, et al. Efficacy and safety of catheter ablation in patients with arrhythmogenic right ventricular dysplasia: a multicenter prospective study. Heart Rhythm. 2018.
Gandjbakhch E, Redheuil A, Pousset F, et al. Clinical outcomes and genetic predictors in arrhythmogenic right ventricular cardiomyopathy: systematic review and meta-analysis. Circ Arrhythm Electrophysiol. 2022.
Medication Comparisons
Compare medications used to treat Arrhythmogenic Right Ventricular Dysplasia 13 C3810138. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy