Arrhythmogenic Right Ventricular Dysplasia 4 C1865881
A serious inherited condition where heart muscle cells are replaced by fatty and fibrous tissue, primarily in the right ventricle. This disrupts normal heart rhythm and can lead to dangerous arrhythmias. Treatment focuses on rhythm control with medications and procedures, and may require an ICD.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Syncope
Chest pain
Ventricular tachycardia
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Arrhythmia episodes
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Beta-Blocker Therapy
Use of beta-blocking agents to reduce heart rate and decrease the heart's workload, helping to prevent arrhythmia triggers. Part of standard first-line pharmacological management for ARVD patients.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
ICD Implantation
Device-based therapy providing continuous rhythm monitoring and automatic defibrillation for life-threatening arrhythmias. Recommended for high-risk patients or those with documented sustained ventricular tachycardia.
Additional treatment options
Competitive Sports Avoidance
Elimination of competitive and endurance athletic participation that places excessive strain on the right ventricle. Replacement with appropriate low-intensity recreational activities.
lifestyleVentricular Tachycardia Ablation
Electrophysiology-guided ablation targeting specific arrhythmia circuits within the right ventricle. Performed when recurrent ventricular tachycardia occurs despite medical therapy.
procedureElectrophysiological Study and Risk Stratification
Invasive cardiac monitoring to induce and map arrhythmia patterns, helping guide treatment decisions and assess sudden death risk. Used selectively based on clinical presentation.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Arrhythmogenic Right Ventricular Dysplasia 4 C1865881?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Marcus WJ, Fowler SB, Taylor HA. Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: Guidelines from the International Task Force. Heart Rhythm. 2020.
Corrado D, Link MS, Thiene G. Arrhythmogenic Right Ventricular Cardiomyopathy: From Genetics to Diagnostic and Therapeutic Challenges. J Am Coll Cardiol. 2018.
Protonotarios N, Tsatsopoulou A, McKoy G. Prospective Long-Term Natural History Study of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy. Circulation. 2021.
Calkins H, Saffitz JE, Cannom DS. Diagnosis and Risk Stratification in Arrhythmogenic Right Ventricular Dysplasia: A Systematic Review and Meta-Analysis. Eur Heart J. 2022.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy