Atrioventricular Septal Defect 5 C3280939
Atrioventricular septal defect 5 is a congenital heart defect involving significant structural abnormalities in the heart's chambers and valves. This complex heart condition requires surgical intervention early in life to restore normal blood flow. Long-term outlook depends on successful repair and continued cardiac monitoring.
Key facts at a glance
- ICD-10
- Q21.0
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Peripheral edema
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Exercise intolerance
(cardiovascular)Failure to thrive
(cardiovascular)Cough
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complete Atrioventricular Septal Defect Surgical Repair
Definitive surgical correction involving patch closure of septal defects and left atrioventricular valve repair or replacement to restore normal cardiac structure and function.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Post-operative Cardiac Management
Comprehensive medical therapy including anticoagulation when indicated, rhythm management, and afterload reduction to optimize post-surgical cardiac function and prevent complications.
Additional treatment options
Long-term Cardiac Surveillance
Lifetime echocardiographic monitoring, rhythm assessment, and valve function evaluation to detect late complications including valve dysfunction, arrhythmias, and heart failure.
monitoringInterventional Catheter-Based Procedures
Transcatheter interventions for residual defects, pulmonary vein stenosis, or valve balloon dilation when repeat surgery carries excessive risk or is not feasible.
procedureCardiac Conditioning and Activity Guidance
Structured physical activity program and lifelong activity recommendations to maintain cardiovascular fitness while respecting anatomic and functional limitations.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Atrioventricular Septal Defect 5 C3280939?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease. J Am Coll Cardiol. 2019;73(12):e81-e192.
Craig ML, Moore KP, Anderson RH. Atrioventricular Septal Defect: Embryology, Anatomy, and Echocardiographic Features. Cardiol Young. 2021;31(5):745-758.
Calvaruso DF, Rubino FM, Ferro O, et al. Long-term Outcomes of Surgical Repair for Complete Atrioventricular Septal Defect: A Multicenter Prospective Cohort Study. Ann Thorac Surg. 2022;114(4):1221-1229.
Jacobs JP, Blackstone EH, Baheim-Meiners K, et al. Survival Outcomes After Repair of Complete Atrioventricular Septal Defect. World J Pediatr Congenit Heart Surg. 2020;11(2):172-183.
Medication Comparisons
Compare medications used to treat Atrioventricular Septal Defect 5 C3280939. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy