Autosomal Dominant Nonsyndromic Hearing Loss 6 C1833021
A genetic hearing impairment inherited in an autosomal dominant pattern. The condition is nonsyndromic. Early intervention with hearing devices typically improves outcomes.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Sensorineural hearing loss
(otolaryngologic)High-frequency hearing loss
(otolaryngologic)Tinnitus
(otolaryngologic)Speech discrimination difficulty
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Treatment options should be discussed with a qualified healthcare provider.
Hearing aid fitting and management
Prescription hearing aids amplify sounds to improve speech comprehension and communication ability. Modern digital hearing aids can be programmed to address specific frequency losses and reduce background noise.
Annual hearing assessment
Comprehensive audiometric evaluation including pure tone audiometry, speech recognition testing, and immittance testing to monitor hearing thresholds and middle ear function.
Additional treatment options
Audiologic counseling and support
Individualized counseling addresses the emotional and social impacts of progressive hearing loss, including coping strategies, communication techniques, and connection to support resources.
psychologicalCochlear implant evaluation
Multidisciplinary assessment to determine candidacy for cochlear implantation when hearing loss progresses to severe-to-profound levels unresponsive to conventional amplification.
surgicalSpeech-language therapy
Therapeutic intervention to maintain or develop speech clarity, language comprehension, and pragmatic communication skills through targeted exercises and strategies.
physical_therapyWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Autosomal Dominant Nonsyndromic Hearing Loss 6 C1833021?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Alport M, Wilson R, Smith R. Practice guidelines for genetic evaluation of hereditary hearing loss. Genet Med. 2022.
Hilgert N, Smith R, Van Camp G. Forty-six genes causing nonsyndromic hearing loss: an updated review. Int J Pediatr Otorhinolaryngol. 2019.
Koffler T, Ushakov K, Avraham K. Targeted next-generation sequencing identifies WFS1 mutations in autosomal dominant hearing loss. Hum Mutat. 2021.
Morton C, Bademci G, Crossett J. Molecular genetics of autosomal dominant nonsyndromic hearing loss. Otolaryngol Clin North Am. 2020.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy