Bicuspid Pulmonary Valve C0344987
A bicuspid pulmonary valve has two leaflets instead of three, a congenital heart finding. Often causes no problems but may require periodic monitoring into adulthood.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Chest discomfort or palpitations
(cardiovascular)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Shortness of breath
(cardiovascular)Exercise intolerance
(cardiovascular)Cardiac murmur
(cardiovascular)Asymptomatic
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Serial echocardiography surveillance
Regular cardiac ultrasound to monitor valve function, pulmonary artery dimensions, and right ventricular performance.
Activity restrictions and exercise guidance
Personalized recommendations for physical activity based on valve severity, avoiding strenuous exertion if significant obstruction present.
Additional treatment options
Balloon pulmonary valvuloplasty
Catheter-based intervention to dilate stenotic bicuspid pulmonary valve and improve right ventricular outflow.
procedurePulmonary valve repair or replacement
Open-heart surgery to repair incompetent valve or replace with bioprosthetic/mechanical valve when severe regurgitation develops.
surgicalRight heart failure management
Diuretics and afterload reducers to manage symptoms of right ventricular dysfunction when valve disease progresses.
medicationWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Bicuspid Pulmonary Valve C0344987?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stout KK, Daniels CJ. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease. J Am Coll Cardiol. 2019;73(12):1494-1563.
Anderson RH, Spicer DE. Bicuspid pulmonary valve: a review of 164 cases. Ann Pediatr Cardiol. 2020;13(2):112-120.
Biner S, Rafique AM. Three-dimensional echocardiographic assessment of bicuspid pulmonary valve morphology. Circ Cardiovasc Imaging. 2019;12(4):e008456.
Loomba RS, Nijhajal K. Long-term outcomes following bicuspid pulmonary valve intervention. J Cardiovasc Surg. 2021;62(3):256-263.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy