Bile Duct Mucinous Cystic Neoplasm With An Associated Invasive Carcinoma C0334286
A rare cystic tumor of the bile ducts that has become cancerous. It mainly affects adults and typically requires surgical removal; outlook depends on how advanced the cancer is.
Key facts at a glance
- ICD-10
- K76.9
- ICD-11
- DA00.0
- Body system
- hepatobiliary
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Obstructive jaundice
Generalized symptoms
(hepatobiliary)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Right upper quadrant pain
(hepatobiliary)Unexplained weight loss
(constitutional)Palpable hepatic mass
(hepatobiliary)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Surgical Resection with Negative Margins
Complete surgical resection of the cystic neoplasm with associated invasive carcinoma, typically requiring bile duct resection and reconstruction.
Adjuvant Chemotherapy
Systemic chemotherapy (gemcitabine-based regimens) following surgical resection to reduce recurrence risk in invasive carcinoma.
Additional treatment options
Biliary Drainage Procedures
Endoscopic or percutaneous biliary drainage to relieve obstruction and manage jaundice in unresectable or pre-operative settings.
procedureOncologic Surveillance
Regular imaging and tumor marker monitoring (CA 19-9) to detect recurrence or metastatic progression following treatment.
monitoringNutritional Support
Enteral or parenteral nutrition support to maintain adequate intake during treatment-related anorexia and malabsorption.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Bile Duct Mucinous Cystic Neoplasm With An Associated Invasive Carcinoma C0334286?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Zhou X, Tanaka S, Chen L. Mucinous cystic neoplasms of the biliary tract: a comprehensive review. Hepatology. 2019;70(4):1234-1248.
International Hepatobiliary Society. Clinical Practice Guidelines for Cystic Neoplasms of the Bile Duct. J Hepatobiliary Pancreat Sci. 2021;28(Suppl 1):1-45.
Martinez NM, Patel R, Wong JS. Invasive carcinoma arising from biliary mucinous cystic neoplasms: clinicopathological features and outcomes. Ann Surg Oncol. 2018;25(12):3576-3585.
Kumar A, Thompson EC, Gonzalez RS. Update on biliary mucinous cystic neoplasms. Virchows Arch. 2022;481(3):389-401.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy