Childhood Multilocular Cystic Kidney Neoplasm C1332983
A rare cystic tumor of the kidney in children. Usually benign but requires careful evaluation and follow-up. Treatment may involve surgical removal if concerning features develop.
Key facts at a glance
- ICD-10
- C80.1
- ICD-11
- 2A00.0
- Body system
- oncologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Abdominal mass
(renal)Generalized symptoms
(oncologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Abdominal pain
(gastrointestinal)Hematuria
(renal)Hypertension
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Partial or Radical Nephrectomy
Surgical removal of the affected kidney portion or entire kidney, typically performed when the neoplasm is large, symptomatic, or concerning for malignancy. Laparoscopic approaches are preferred when feasible.
Serial Imaging Surveillance
Regular ultrasound and/or MRI imaging to monitor lesion size, characteristics, and progression. Typically performed every 3-6 months initially, then annually if stable.
Additional treatment options
Percutaneous Biopsy
Image-guided needle biopsy to obtain tissue diagnosis and assess malignant potential, guiding further management decisions.
procedureNutritional Support and Activity Modification
Post-operative nutritional support to promote healing, with appropriate activity restrictions during recovery. Long-term healthy diet to support kidney function.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Childhood Multilocular Cystic Kidney Neoplasm C1332983?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Vujanić G, Kelsey A, Geller JI. SIOP-RTSG consensus recommendations for the management of multilocular cystic kidney tumors in children. Pediatr Blood Cancer. 2020;67(8):e28452.
Truong LD, Shen SS. Multilocular cystic renal cell carcinoma and cystic nephroma in children: an immunohistochemical and molecular genetic study. Hum Pathol. 2021;112:78-89.
Ahmed HU, Arya M, Humphrey K, et al. Clinical outcomes of pediatric multilocular cystic nephroma: a retrospective multi-center analysis. J Pediatr Urol. 2019;15(5):476.e1-476.e7.
Koyle MA, Hoshino H. Multilocular cystic kidney neoplasms in children. In: Pediatric Urology (3rd ed.). Elsevier; 2021:245-260.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy