Coenzyme Q10 Deficiency Primary 1 C3551954
Primary coenzyme Q10 deficiency type 1 is a genetic disorder impairing cellular energy production. It often causes neurological and muscular problems. Early diagnosis and Q10 supplementation may help slow progression.
Key facts at a glance
- ICD-10
- E88.9
- ICD-11
- 5A00.0
- Body system
- metabolic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Seizures
Fatigue or weight changes
(metabolic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Encephalomyopathy
(Neurological)Retinopathy
(Ophthalmic)Nephrotic syndrome
(Renal)Medication Comparisons
Compare medications used to treat Coenzyme Q10 Deficiency Primary 1 C3551954. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy