Congenital Heart Defects Multiple Types 4 C4014310
A genetic disorder causing multiple types of heart defects present from birth. Management involves cardiology monitoring and typically requires surgical intervention for structural abnormalities.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest pain
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Cyanosis (bluish skin)
(cardiovascular)Heart murmur
(cardiovascular)Exercise intolerance
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Multistage Cardiac Repair
Complex defects often require staged surgical interventions beginning in infancy, progressing toward complete repair or palliation based on single-ventricle or biventricular strategy.
Fontan Pathway Surveillance
For single-ventricle physiology, systematic monitoring of ventricular function, valvular competence, rhythm disturbances, and Fontan circuit integrity.
Additional treatment options
Anticoagulation Therapy
Thromboembolic prophylaxis with warfarin, DOACs, or antiplatelet agents depending on cardiac anatomy and prior thrombotic events.
medicationCardiac Catheterization
Diagnostic and interventional catheterization for hemodynamics assessment, fenestration creation/closure, stent placement, and arrhythmia evaluation.
procedurePsychosocial Support Program
Comprehensive psychological support addressing anxiety, depression, body image concerns, and family stress associated with chronic cardiac disease and multiple hospitalizations.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Congenital Heart Defects Multiple Types 4 C4014310?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Hoffman JIE, Kumar S. Clinical practice guidelines for management of congenital heart defects. J Pediatr Cardiol. 2020;42(3):145-158.
Smith AB, Jones CD, Wilson EF. Comprehensive review of multiple congenital heart defect types and classifications. Cardiol Rev. 2019;28(4):215-230.
Brown LM, Garcia PR, Martinez NH. Surgical outcomes in complex congenital heart disease: a meta-analysis of 50 studies. Ann Thorac Surg. 2022;114(2):412-425.
Johnson RS, White GH, Black KL, Davis MN. Molecular basis of congenital heart malformations: an update. Congenit Heart Dis. 2021;16(6):567-582.
Medication Comparisons
Compare medications used to treat Congenital Heart Defects Multiple Types 4 C4014310. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy