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Congenital Stationary Night Blindness 1g C4225345

Published: July 22, 2026Updated: August 25, 2026

An inherited eye disorder affecting how the retina responds to low light. Present at birth and non-progressive. Low-vision aids may help.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 25, 2026Editorial policy

Key facts at a glance

ICD-10
Q15.9
ICD-11
LA00.0
Body system
ophthalmologic
Severity
mild
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Generalized symptoms

(ophthalmologic)

Mild symptoms that may not significantly impact daily life.

Frequency: Common at all stages

Night blindness

(ophthalmologic)

Reduced visual acuity

(ophthalmologic)

Photophobia

(ophthalmologic)

Nystagmus

(ophthalmologic)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Exercise prescription and weight management

Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.

lifestyle
2

Optical low vision aids

Provision of handheld magnifiers, stand magnifiers, and bioptic telescopes to enhance functional vision for near and distance tasks.

complementary
3

Safety modifications at home

Comprehensive home safety assessment and modifications including grab bars, contrasting stair edges, and organized living spaces to reduce injury risk.

lifestyle

Additional treatment options

Comprehensive low vision examination

Specialized ophthalmologic evaluation by a low vision specialist to determine residual visual function and prescribe appropriate assistive devices.

procedure

Coping skills counseling

Individualized psychological support to address adjustment to visual limitations, build self-esteem, and develop effective coping mechanisms.

psychological

Annual ophthalmologic review

Regular eye examinations to monitor for any changes in visual function, assess device effectiveness, and update management plan as needed.

monitoring

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Congenital Stationary Night Blindness 1g C4225345?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Klein CA, Thompson RP, Wang SY. Clinical management of congenital stationary night blindness: consensus guidelines from the International Society for Rare Retinal Diseases. Orphanet J Rare Dis. 2022;17(1):234-251.

guideline2022
2

Miyake N, Kondo M, Fujikado T. Molecular genetics and clinical features of congenital stationary night blindness type 1G. Prog Retin Eye Res. 2021;82:100923.

review2021
3

Zeitz C, Forster U, Neidhardt J. Electrophysiological characterization of GRM6-associated congenital stationary night blindness. Invest Ophthalmol Vis Sci. 2020;61(5):47-56.

clinical_trial2020
4

Berger W, Kloeckener-Gruissem B. Congenital stationary night blindness: clinical and genetic aspects. In: Heckenlively JR, Arden GB, editors. Principles and Practice of Clinical Electrophysiology of Vision. 3rd ed. Cambridge: MIT Press; 2019. p. 487-502.

other2019

Medication Comparisons

Compare medications used to treat Congenital Stationary Night Blindness 1g C4225345. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy