Coronal Synostosis Syndactyly And Jejunal Atresia C2931194
A rare birth disorder affecting skull, hand, and intestinal development. Requires surgical repair of skull bones, finger webbing, and intestinal blockage. Complex care involving multiple specialists.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Jejunal atresia
Generalized symptoms
(congenital)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Coronal synostosis with abnormal head shape
(congenital)Syndactyly of fingers
(congenital)Hearing loss
(ear)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Craniofacial Reconstruction Surgery
Surgical intervention to release coronal synostosis and reconstruct affected skull structures, typically performed in early infancy.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Syndactyly Release Procedure
Surgical separation of webbed fingers with skin grafting and functional rehabilitation to improve hand use and dexterity.
Additional treatment options
Jejunal Atresia Surgical Repair
Surgical correction of jejunal atresia to restore intestinal continuity and function, typically performed shortly after diagnosis.
surgicalDevelopmental and Growth Monitoring
Regular assessment of developmental progress, growth parameters, and neurological development with early intervention referrals.
monitoringHand Function Rehabilitation
Post-surgical hand therapy program including range of motion exercises, strength training, and functional activities to maximize hand use.
physical_therapyWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Coronal Synostosis Syndactyly And Jejunal Atresia C2931194?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy