Developmental And Epileptic Encephalopathy 74 C5193074
A severe developmental and epileptic encephalopathy with early-onset seizures and limited developmental progress. Treatment involves seizure management and multidisciplinary support.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Epileptic seizures
Status epilepticus
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Motor developmental delay
(neurologic)Cerebellar atrophy
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Anti-seizure medication therapy
Comprehensive seizure management through anti-epileptic drugs tailored to the patient's specific seizure types and tolerability profile.
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Ketogenic diet therapy
High-fat, low-carbohydrate diet that may help reduce seizure frequency through metabolic mechanisms affecting neuronal excitability.
Additional treatment options
Early intervention physical therapy
Structured motor development program addressing hypotonia, coordination, and movement patterns typical in developmental encephalopathies.
physical_therapyContinuous EEG-video monitoring
Inpatient monitoring to characterize seizure types, identify epileptiform activity patterns, and guide medication adjustments.
monitoringNeuropsychological evaluation and support
Comprehensive cognitive and behavioral assessment to identify strengths, challenges, and appropriate educational interventions.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Developmental And Epileptic Encephalopathy 74 C5193074?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Developmental And Epileptic Encephalopathy 74 C5193074. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy