Developmental And Epileptic Encephalopathy 77 C5231405
A rare developmental and epileptic encephalopathy causing severe seizures and limited developmental progress in infancy. Management includes anticonvulsants and supportive care.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Seizures
(neurologic)Hypotonia
(neurologic)Microcephaly
(neurologic)Visual impairment
(ophthalmic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Precision anti-seizure pharmacotherapy
Targeted medication selection based on identified genetic cause when possible, with careful titration and monitoring for optimal response.
Functional mobility and independence program
Therapeutic exercises and adaptive techniques to maintain joint mobility, prevent contractures, and maximize functional abilities.
Additional treatment options
Regular seizure and development tracking
Systematic logging of seizure frequency, duration, and characteristics combined with developmental milestone monitoring.
monitoringFamily education and respite support
Comprehensive caregiver training on seizure first aid, emergency management, and stress reduction combined with respite care access.
lifestyleBalanced nutritional support therapy
Ensuring adequate caloric intake, hydration, and micronutrients while considering any specific dietary triggers or beneficial modifications.
dietaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Developmental And Epileptic Encephalopathy 77 C5231405?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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Medically reviewed by WellAlly Editorial Team Last reviewed August 26, 2026. · Read our editorial policy