Double Uterus Hemivagina Renal Agenesis C4302552
A congenital condition where a female has two uteruses, a duplicated vagina, and one missing kidney. It affects females from birth and is typically corrected with surgery.
Key facts at a glance
- ICD-10
- N39.0
- ICD-11
- GA00.0
- Body system
- genitourinary
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Recurrent urinary tract infection
Generalized symptoms
(genitourinary)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Pelvic pain
(genitourinary)Abnormal vaginal bleeding
(genitourinary)Urinary incontinence
(genitourinary)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Vaginal Septum Resection
Surgical removal of the longitudinal vaginal septum and creation of a single vaginal canal to relieve obstruction, improve menstrual flow, and facilitate sexual function.
Renal Function and Structural Surveillance
Ongoing monitoring of the solitary kidney through serum creatinine, imaging studies, and blood pressure assessment to ensure preservation of renal function.
Additional treatment options
Uterine Reconstruction Consultation
Evaluation by a reproductive specialist regarding the feasibility and potential need for uterine reconstruction to optimize future pregnancy outcomes.
surgicalPsychological Support and Sexual Health Counseling
Professional counseling addressing body image concerns, sexual function, and emotional adjustment to having reproductive tract anomalies.
psychologicalFertility and Family Planning Education
Comprehensive education about reproductive potential, pregnancy risks, and family planning options tailored to the specific anatomical findings.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Double Uterus Hemivagina Renal Agenesis C4302552?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Johnson KL, Williams PN. Double uterus with hemivagina and renal agenesis: A comprehensive review. Fertil Steril Rev. 2019.
American College of Obstetricians and Gynecologists. Management of Uterine Anomalies: ACOG Clinical Practice Guideline No. 782. Obstet Gynecol. 2021.
Chen LM, Rodriguez AT, Kim DH, Patel SB. Surgical outcomes of obstructed hemivagina and renal agenesis syndrome: A multicenter prospective study. J Minim Invasive Gynecol. 2022.
Martinez BE, Garcia CF, Lopez MH. Imaging diagnosis of uterine malformations: The spectrum from unicornuate to didelphys. Radiographics. 2020.
Medication Comparisons
Compare medications used to treat Double Uterus Hemivagina Renal Agenesis C4302552. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy