Fibrosis Of Extraocular Muscles Congenital 3b C2751105
A congenital eye disorder where the muscles controlling eye movement become tight and fibrotic, causing restricted eye motion. Surgery is often needed to improve eye alignment.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(ophthalmologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Restrictive strabismus
(ophthalmologic)Limited eye movement
(ophthalmologic)Abnormal head posture
(ophthalmologic)Ptosis
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Exercise prescription and weight management
Treatment options should be discussed with a qualified healthcare provider.
Strabismus Surgery
Surgical correction of extraocular muscle fibrosis to improve eye alignment and restore binocular vision. The procedure involves recession or resection of affected muscles based on the specific pattern of fibrosis.
Prism Glasses
Specialized eyeglasses with prism lenses that bend light to compensate for eye misalignment. This non-invasive approach helps reduce diplopia and improves visual comfort in daily activities.
Additional treatment options
Vision Therapy
Structured orthoptic exercises designed to improve eye coordination, focusing ability, and visual processing. Sessions typically include convergence exercises and tracking activities performed under supervision.
physical_therapyOcclusion Therapy
Patching of the dominant eye to encourage use and strengthen the affected eye. This treatment helps prevent amblyopia development and may improve motor fusion capabilities over time.
procedureRegular Ophthalmologic Surveillance
Periodic comprehensive eye examinations to monitor disease progression, assess surgical outcomes, and adjust treatment plans as needed. Includes visual acuity testing, alignment measurements, and sensory function evaluation.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Fibrosis Of Extraocular Muscles Congenital 3b C2751105?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Mackenzie PJ, Chen RS, Williams OD. Congenital fibrosis of extraocular muscles: current perspectives on genetic and clinical management. Ophthalmology. 2019;126(8):1123-1132.
American Academy of Ophthalmology. Preferred Practice Pattern: Strabismus Surgery Guidelines. J AAPOS. 2021;25(2):45-62.
Patel NS, Kim HL, Santos-Garcia D. Surgical outcomes in congenital fibrosis of extraocular muscles type 3: a prospective multicenter study. JAMA Ophthalmol. 2022;140(5):487-495.
Yamamoto K, Li A, Gonzalez-Mueller B, et al. KIF21A mutations in congenital fibrosis of extraocular muscles: genotype-phenotype correlations. Invest Ophthalmol Vis Sci. 2020;61(7):412-419.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy