Glaucoma 3 Primary Congenital A Digenic C1866550
Primary Congenital Glaucoma 3A is a severe inherited eye disorder causing abnormally high eye pressure from birth. It affects the optic nerve and can lead to vision loss if untreated. Early surgery is often needed to preserve vision.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Buphthalmos
Corneal clouding
Excessive tearing
(ophthalmologic)Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Photophobia
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Combination drug regimen with regular assessment
Active treatment with regular monitoring by a healthcare provider is recommended.
Goniotomy
A surgical procedure where a tiny incision is made in the trabecular meshwork to improve aqueous humor drainage and reduce intraocular pressure. This is often the preferred surgical approach for congenital glaucoma when the cornea is clear enough to visualize the angle.
Topical Beta-Blockers
Eye drops that reduce aqueous humor production by blocking beta-adrenergic receptors in the ciliary body. Used as adjunctive therapy before or after surgery to control intraocular pressure.
Additional treatment options
Trabeculectomy with Mitomycin C
A filtering surgery that creates a new drainage pathway for aqueous humor, often combined with antimetabolite application to prevent scar tissue formation. Reserved for cases where angle surgery fails or is not feasible.
surgicalTopical Prostaglandin Analogs
Medications that increase uveoscleral outflow of aqueous humor, lowering intraocular pressure through a different mechanism than beta-blockers. Often used in combination therapy.
medicationRegular Ophthalmologic Surveillance
Ongoing comprehensive eye examinations including intraocular pressure measurement, corneal diameter assessment, and optic nerve evaluation to detect progression or complications early.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Glaucoma 3 Primary Congenital A Digenic C1866550?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy